XI./2.1.: Funnel chest (pectus excavatum) XI./2.1.1. Definition XI./2.1
Transcription
XI./2.1.: Funnel chest (pectus excavatum) XI./2.1.1. Definition XI./2.1
XI./2.1.: Funnel chest (pectus excavatum) XI./2.1.1. Definition Thoracic deformity with inward displacement of the sternum. XI./2.1.2. Etiology Sporadic and genetic factors play a role in the development of funnel chest. XI./2.1.3. Clinical features Total or partial, symmetrical or asymmetrical inward displacement of the sternum. The sternal end of the ribs and the lower part of the chest are also often affected. It is already noticeable during the first year of life. Usually thin, asthenic children, if the deformity is greater, patients are characteristically less sturdy and more prone to fatigue. A deformity with over 50% reduction of the thoracic anteroposterior diameter can lead to major cardiorespiratory symptoms and paradox breathing may occur. Figure 1.: Clinical appearance of funnel chest XI.2.1.4. Investigations Radiographs: lateral chest X-ray should be performed in case of major deformity, and the extent of displacement - thoracic AP diameter ratio should be evaluated. AP and lateral spine X-rays should be performed in adolescence if associated spinal deformity is suspected. ECG, exercise ECG, echocardiography, and lung function tests in case of significant deformity, lung problems and weakness. XI./2.1.5. Associated diseases Scheuermann’s disease (the child „hides” his chest deformity by adopting a hyperkyphotic posture), scoliosis, prune belly syndrome. XI./2.1.6. Treatment Conservative treatment: strengthening of the chest and trunk muscles, breathing exercises, spinal exercises in adolescence (prevention of spinal deformities). Surgery: restricted cardiopulmonary function is an absolute indication for sugery. Psychological burden is considered a relative indication at the end of puberty based on the child's own decision. Nuss surgery (thoracoscopic method, where a rigid pre-bent metal bar is fixed to the inner wall of the chest to correct the deformity; the implant should be removed after 2-3 years). Figure 2.: Funnel chest correction according to Nuss. The position of the implant seen on a postoperative AP chest X-ray Literature Obligatory literature Miklós Szendrői: Orthopedics Chapter 24.10.